Teaching NeuroImages: Adrenoleukodystrophy presenting as raised intracranial pressure
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چکیده
منابع مشابه
Teaching NeuroImages: adrenoleukodystrophy presenting as raised intracranial pressure.
A 7-year-old boy presented with acute onset headache, vomiting, and visual deterioration 2 weeks previously without any cognitive or behavioral changes. Optic fundi showed papilledema, and there were no pyramidal signs or gait disturbances. The remainder of the neurologic examination was normal. CSF protein was 174 mg/dL. Although MRI features (figure) were consistent with adrenoleukodystrophy ...
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Five patients are described in whom a benign or malignant thoracolumbar tumour, producing increased level of cerebrospinal fluid protein, was associated with hydrocephalus or papilloedema or both. A review of the clinical and laboratory features in these and 40 published cases underlines the difficulty in explaining the increased intracranial pressure in such patients. Slow absorption of cerebr...
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Raised intracranial pressure (ICP) is a common problem in neurosurgical and neurological practice. It can arise as a consequence of intracranial mass lesions, disorders of cerebrospinal fluid (CSF) circulation, and more diffuse intracranial pathological processes. Its development may be acute or chronic. There are well established methods for the measurement, continuous monitoring, and treatmen...
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ژورنال
عنوان ژورنال: Neurology
سال: 2010
ISSN: 0028-3878,1526-632X
DOI: 10.1212/wnl.0b013e3181e042b2